Our experience in the treatment of a patient with ectopia cordis


Published: Jun 30, 2025
Keywords:
ectopia cordis, neonate, cardiac surgical correction
ALMIRA KADIC
Mirza Halimic
Zijo Begic
Selma Dizdar
Semra Cepic Kapic
Abstract

Ectopia cordis (EC) is a rare congenital anomaly when part or entire heart is located outside the. thoracic cavity. It may occur isolated or as part of multiple defects. A male term neonate was transported to our Neonatal Intensive Care Unit (NICU) immediately after vaginal delivery. A significant defect was noted on the anterior thoracic wall with an ectopia cordis (EC). EC was immediately protected with sterile gauze, sterile saline solution and surgical sterile bags. The newborn was treated with antibiotics, radiological exams were performed, followed by four stage surgically treatment which including ligation of PDA, reconstruction of the thoracic wall, mediastinal antimicrobe irrigation, sternum osteosynthesis, and secondary skin graft. Tracheostomy was also necessary.
The surgical wound healed without complications. The newborn is now 4 months old, breathing through a tracheostomy tube. The baby is fed via NG tube, and progress in body weight is satisfactory. Echocardiogram follow-ups show satisfactory results. The neonate is on diuretics and beta-blockers and is being monitored by a multidisciplinary team. Prenatal diagnosis is crucial for the initial management of EC. Surgical management is individualized. A multidisciplinary approach is needed for monitoring and treatment due to several postoperative complications.

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Author Biographies
Mirza Halimic, pediatric cardiologist

Pediatric Clinic, Clinical Center University of Sarajevo

Zijo Begic, pediatric cardiologist

Pediatric Clinic, Clinical Center University of Sarajevo

Selma Dizdar, Pediatric cardiologist

Pediatric Clinic, Clinical Center University of Sarajevo

Semra Cepic Kapic, Pediatric cardiologist

Pediatric Clinic, Clinical Center University of Sarajevo

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